A Case of Osteogenesis Imperfecta (Fragilitas Ossium)
نویسنده
چکیده
A girl, N. G., aged 8 years, reported for a radiologic^ 'examination of her right forearm and wrist. The history given was that the child had slipped and fallen on her hand, an accident which the parents witnessed and which, in their opinion, was quite a trivial injury and out of proportion to the deformity of the hand caused by it. , On rr-ray examination it was found that she hacI sustained a fracture of the lower third of the radius with some backward displacement. Reduction of fracture was eas}', and with massage and movements the result was good. _ ,
منابع مشابه
Osteogenesis Imperfecta Tarda. A Review with Case Reports
S. |NIYOGI, m.b. (Cal.) Surgical Registrar,"Nilratan Sarkar Medical College Hospitals, Calcutta Osteogenesis imperfecta tarda is one variety a clinical syndrome which has been given various names such as fragilitas ossium, idiopathic osteopsathyrosis, periosteal dysplasia, etc. Thomson (1921) divided it into two broad clinical types?preand post-natal. Pre-natal cases are more severe and often t...
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elicited in both families as complete family history was not available, but a strong familial tendency of the disease was suggested. The cardinal triad (blue sclera, deafness and brittle bones) was not seen in all cases, while the blue sclera was reported as consistent finding. The combination of blue sclera and fracture was more common as compared to deafness. Among the 7 cases reported, 2 fit...
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attract attention : still more, when this remarkable condition afflicts several members of one family, which is further distinguished by a startling blueness of what in others is " the white of the eye". Yet, although the condition is by no means rare, the first recognizable account appeared in 1788, when Eckman1 described a family, three generations of which suffered from multiple fractures. N...
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